Fig. 2

The first color fundus photography (a) demonstrates the presence of a subfoveal choroidal neovascularization in a patient with angioid streaks due to Pseudoxantoma elasticum (Group 1). The second case (b) shows pigmentary changes associated to angioid streaks (Group 2). The third case (c) evidences the presence of angioid streaks without other association (Group 3). The retinal and choroidal thickness maps (d–i) evidence in all cases a normal topographic distribution. The swept-source OCT horizontal scan centered in the fovea in the first case (j) shows the presence of a subretinal fibrosis with no signs of exudative activity; the second scan (k) shows the presence of subretinal fluid associated with pigment migration; the third scan (l) shows a normal macular anatomy and the absence of NV or SRF