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Table 1 Updated classification system

From: Multi-modal imaging and anatomic classification of the white dot syndromes

Uveitic syndromes with choroidal-based pathology

 Sympathetic ophthalmia

Systemic uveitic syndromes with choroidal-based pathology

 Vogt–Koyanagi–Harada disease

 Sarcoidosis

Multifocal choroiditis with outer retinal/choriocapillaris-based pathology

 Without vitritis

  Histoplasmosis

  Punctate inner choroidopathy

 With vitritis

  Multifocal choroiditis with panuveitis

  Multiple evanescent white dot syndrome

  Acute posterior multifocal placoid pigment epitheliopathy

  Serpiginous choroiditis

  Relentless placoid chorioretinitis

  Birdshot chorioretinopathy

Neoplastic

 Primary uveal lymphoma

 Primary vitreoretinal lymphoma

 Secondary (metastatic) Lymphoma

Infectious

 Syphilis

 Tuberculosis

 Lyme disease