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Table 1 Revised FEVR clinical staging system 2014 and number of eyes

From: Familial exudative vitreoretinopathy in a 4 generations family of South-East Asian Descendent with FZD4 mutation (c.1501_1502del)

Stage

Description

No. of eyes

1

Avascular periphery or anomalous intraretinal vascularization

 

1A

Without exudate or leakage

1

1B

With exudate or leakage

0

2

Avascular retinal periphery with extraretinal vascularization

 

2A

Without exudate or leakage

2

2B

With exudate or leakage

1

3

Extramacular retinal detachment

 

3A

Without exudate or leakage

2

3B

With exudate or leakage

1

4

Macula-involving retinal detachment, subtotal

 

4A

Without exudate or leakage

3

4B

With exudate or leakage

0

5

Total retinal detachment

 

5A

Open funnel

0

5B

Closed funnel

10