Table 2 Revised familial exudative vitreoretinopathy clinical staging system [37]

1

Avascular periphery or anomalous intraretinal vascularization

 1a

Without exudate or leakage

 1b

With exudate or leakage

2

Avascular retinal periphery with extraretinal vascularization

 2a

Without exudate or leakage

 2b

With exudate or leakage

3

Extramacular retinal detachment

 3a

Without exudate or leakage

 3b

With exudate or leakage

4

Macula-involving retinal detachment

 4a

Without exudate or leakage

 4b

With exudate or leakage

5

Total retinal detachment

 5a

Open funnel

 5b

Closed funnel