From: Autoimmune retinopathy: findings and limitations from optical coherence tomography angiography
Patient | Age | Gender | Eye | BCVA | Systemic diseases | Treatment | Antibodies | Additional AIR diagnostic criteria |
---|---|---|---|---|---|---|---|---|
Control 1 | 85 | Female | OD | 20/25 | None | None | Not done | |
Control 2 | 64 | Male | OD | 20/20 | None | None | Not done | |
Control 3 | 74 | Male | OD | 20/25 | None | None | Not done | |
Control 4 | 69 | Female | OD | 20/25 | None | None | Not done | |
Control 5 | 49 | Female | OD | 20/20 | None | None | Not done | |
AIR 1 | 89 | Female | OS | CF at 3’ | None | Azathioprine | Not done | Diffuse retinal atrophy, flat ffERG, normal vision prior to onset, rapid progression of visual field loss, subtle “flying saucer sign” |
AIR 2 | 49 | Female | OS | 20/20 | Multiple sclerosis | Mycophenolate azathioprine | 22, 30, 42, 44, 62, 72, 136 kDa | Diffuse peripheral retinal atrophy, rapid progression of visual field loss, photopsias, classic OCT “flying saucer sign” |
AIR 3 | 76 | Female | OD | 8′/200 | Hashimoto’s thyroiditis | Mycophenolate | 30, 45, 46 kDa | Decreased amplitudes on ffERG and mfERG, rapid progression of visual field loss, photopsias, subtle “flying saucer sign” |
CAR 4 | 79 | Female | OD | 20/40 | PMR, Hypothyroid, Breast Cancer | Observation | 30, 46 kDa | Flat ffERG, rapid progression of visual field loss |
AIR 5 | 75 | Female | OS | LP | Hypothyroidism, RA | Observation | 30, 33, 60, 70 kDa | Reduced → flat ffERG, photopsias, normal vision prior to onset, rapid progression of visual field loss until LP |